Diffuse plane xanthomatosis in a patient withBudd-Chiari syndromeand monoclonal gammopathy
نویسندگان
چکیده
منابع مشابه
Diffuse plane Xanthomatosis: A case report
A 58-year-old man had 3 years history of asymptomatic, extensive, yellowish patches on his face, neck, trunk and arms. Histopathological examination confirmed the diagnosis of diffuse plane xanthomatosis. This is a rare non-lipemic disease in which xanthomatous lesions develop in the skin in association with paraproteinemia. Serum lipids are usually normal. The histological features include bot...
متن کاملDiffuse normolipemic plane xanthoma associated with monoclonal gammopathy.
Diffuse normolipemic plane xanthoma (DNPX) was first described by Altman and Winkelmann in 1962. It is a rare and non-inherited form of xanthomatosis. Clinically, the dermatosis is characterized by the presence of symmetric yellowish-orange plaques that favor the neck, upper trunk, flexural folds and periorbital region. It has been recognized to be associated with hematological diseases, especi...
متن کاملPathogenesis and treatment of xanthomatosis associated with monoclonal gammopathy.
Xanthomas are a common manifestation of lipid metabolism disorders. They include hyperlipemic xanthoma, normolipemic xanthoma, and a related condition, necrobiotic xanthogranuloma (NXG). All 3 forms can be associated with monoclonal immunoglobulin (MIg). In an attempt to improve diagnosis, understanding, and treatment of this association, we retrospectively analyzed a personal series of 24 pati...
متن کاملDiffuse pulmonary amyloidosis with monoclonal IgG-kappa gammopathy.
A 62-year-old female with diffuse pulmonary amyloidosis developed abnormal radiographic findings while under observation for hyperimmunoglobulinemia over a ten-year period. Serum immunoglobulin G (IgG) was elevated (4,620 mg/dl), and associated with monoclonal gammopathy (M protein) of the kappa type, but no evident abnormalities were apparent in bone marrow. Chest radiograph and computed tomog...
متن کاملDiffuse normolipemic plane xanthomas in a healthy male infant
Diffuse normolipemic plane xanthoma is characterized by thepresence of yellowish-orange plaques on the eyelids, neck, uppertrunk, buttocks and flexural surfaces of the extremities in patientswith a normal lipid profile. It mainly affects adults of both sexes.Diffuse normolipemic plane xanthomas are usually associatedwith reticuloendothelial system disorders, such a...
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ژورنال
عنوان ژورنال: Indian Journal of Dermatology
سال: 2009
ISSN: 0019-5154
DOI: 10.4103/0019-5154.57616